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2.6.1.40 |
Description |
(R)-3-amino-2-methylpropionate--pyruvate aminotransferase. |
Alternative names |
D-3-aminoisobutyrate--pyruvate aminotransferase; Beta-aminoisobutyrate--pyruvate transaminase. |
Catalyzed reaction |
(R)-3-amino-2-methylpropanoate + pyruvate = 2-methyl-3-oxopropanoate + L-alanine. |
Cofactor |
Pyridoxal-phosphate. |
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The enzyme from rat liver appears to be identical to Alanine--glyoxylate aminotransferase (2.6.1.44), isoenzyme 2. |
Diseases |
Hyper-beta-aminoisobutyricaciduria |
Organisms |
-Metazoa -Human |
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Links |
Enzyme (activities) 2.6.1.40
BRENDA (activities) 2.6.1.40
KEGG (pathways) 2.6.1.40
PLPMDB (PLP mutants) 2.6.1.40
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References |
Articles on 2.6.1.40 |
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last changed |
2009/07/07 14:56 |
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