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B6db activities:
Description (R)-3-amino-2-methylpropionate--pyruvate aminotransferase.
Alternative names D-3-aminoisobutyrate--pyruvate aminotransferase;
Beta-aminoisobutyrate--pyruvate transaminase.
Catalyzed reaction (R)-3-amino-2-methylpropanoate + pyruvate = 2-methyl-3-oxopropanoate + L-alanine.
Cofactor Pyridoxal-phosphate.
The enzyme from rat liver appears to be identical to Alanine--glyoxylate aminotransferase (, isoenzyme 2.
Diseases Hyper-beta-aminoisobutyricaciduria
Organisms -Metazoa -Human
Links Enzyme (activities)
BRENDA (activities)
KEGG (pathways)
PLPMDB (PLP mutants)
 Kontani, Y.; Kaneko, M.; Kikugawa, M.; Fujimoto, S.; Tamaki, N. (1993) Identity of D-3-aminoisobutyrate-pyruvate aminotransferase with alanine- glyoxylate aminotransferase 2 Biochim Biophys Acta 1156 161-6.

Articles on
last changed 2009/07/07 14:56

B6db activities